52 year old lady presented with phobia, visual hallucinations from 1 month, progressive cognitive decline, rigidity, abnormal posturing of limbs from 10 days, startle response to sound, myoclonic jerks, pseudobulbar affect, bladder and bowel incontinence from 1 week. No h/o fever.

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Progressive supranuclear palsy The cardinal manifestations of PSP are as follows: Supranuclear ophthalmoplegia Pseudobulbar palsy Prominent neck dystonia Parkinsonism Behavioral, cognitive, and gait disturbances that cause imbalance Frequent falls/impaired postural reflexes

Creutzfeldt–Jakob disease

More specifically variant CJD

its CJD

leucoencephalopathy

myoclonic jerks r very characteristic of sspe..may b subacute sclerosing panencephalitis

Clue is in characteristic MRI n EEG..
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