Baby delivered through nvd.cried immediately after birth,sudden

Baby delivered through NVD.cried immediately after birth,sudden developed respiratory distress.O/e retrognathia with glossoptosis and cleft palate were seen. Comment on diagnosis and early management.

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PIERRE ROBBINS SYNDROME TREATMENT The goals of treatment in infants with Robin sequence focus upon breathing and feeding, and optimizing growth and nutrition despite the predisposition for breathing difficulties. If there is evidence of airway obstruction (snorty breathing, apnea, difficulty taking a breath, or drops in oxygen), then the infant should be placed in the sidelying or prone position,

NVD, weight of the Infant ! Looks like FACE-PRESENTATION. CONGESTED FACE +, SWOLLEN NOSE + MICRO-NAGTHIA + IMPRESSION : DIFFICULT NVD WITH FACE PRESENTATION. SEATCH FOR OTHER CONGENITAL ANOMALIES. DX : CLEFT-PALATE WITH PIERRE-ROBIN-SEQUENCE. RX : PRONE-POSTURE TO AVOID GLOSSOPTOSIS. FEEDING EBM WITH "CUT-NIPPLE" PEDIATRIC SIRGEONS CONSULTATION.

D/D 1)Pierre Robin syndrome - cleft palat , retrognathia, glossoptosis 2)Stickler syndrome characterized by a short mandibular ramus, antegonial notching of the mandibular body, myopia, and joint problems. 3)Velocardiofacial syndrome is characterized by a retrognathic mandible, palatal abnormalities, hypotonia, impaired thymus development, and cardiac malformation.. Above case look like PRS Management- Prone or lateral positioning will solve the airway obstruction  If the baby continues to show evidence of desaturation, then placement of a nasopharyngeal (NP) tube is indicated Early feeding via nasogastric tube Recently, it has been reported that severe PRS babies can have low urinary sodium.Sodium supplementation in such babies with low urinary sodium improved their weight gain and reversed the tendency to failure to thrive.

Pierobbins syndrome .kept baby prone position cautious feeding pads surgery opinion.risk of aspiration.

Micrognathia. Respiratory distress may be due to glosoptosis. Adv. Proper positioning of baby Feeding

Pierre Robin with face presentation, prone position or lateral position and feeding with either spoon or cut nipple till palate mould can be practical solution Surgery at approximately 3-4 months

Pierre Robin with face presentation.. Agree with Dr. Minol Amin
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Pierre Robbins syndrome with difficult labour. Respiratory difficulties and feeding problem should be taken care of in nicu in prone position. Avoid tounge fall by giving a suture bite on anterior portion of tounge and little traction outside if needed and N G tube feeding.

Retrognathia, increased intercanthal distance, cleft palate...Investigation-- Usg Abdomen & KUB.. EChO.. D/D--- pierre robbin syndrome, patau ( after full examination)

Clear the air way properly.and nicu care and.cleft palate' s Surgery with in 6 month..pediatric expert opinion for further management plz.

Pierre robins syndrome
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Pierre Robin Syndrome

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