Spotters , 19/m, deformity, abnormal mobility of forearm since 2003. But no pain, has multiple subcutaneous nodules on Palpatine and hyper pigmented patches over back and thigh. Diagnosis and management

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Thank you Dr Anup Dr Vaishali, Dr Sameer, DrUmesh , Dr Vijay. It is congenital Psudoarthrosis of Forearm bone, which is commonly associated with neurofibromatosis(%I don't remember but certainly more than 50%of cases, operated =fusion of prox ulna with distal radius with corticocancellus bone graft from ipsilateral ilium. And fixed with lcp. Was searching for its incidence. Will share few papers.

Description fit neurofibromatosis with pseudoarthrosis of both bones forearm Skeletal survey for other long bones Reconstruction a real challenge Restoration of function than restoration of Anatomy

Congenital pseudoarthrosis of forearm bones. Occurs in neurofibromatosis.

Pseudoarthrosis forearm bones following neutrofibromatosis trt is illizrov

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Ulnar and radial pseudarthrosis,malalignment, radial head dislocation resorption of distal ulnar shaft. These findings in the presence of subcutanoues nodules and hyperpigmented patches go in favour of Neurofibromatosis type 1

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neurofibromatosis. i donot have any experience of such complicated cases.

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Nonoperative bracing in clamshell orthosis or patellar tendon bearing orthosis indications Children of ambulatory age (weight bearing) bowing without pseudarthrosis pontaneous remodeling is not expected goal is to prevent further bowing and fractures osteotomy for bowing alone is contraindicated technique maintained until skeletal maturity Operatives urgical fixation indication bowing with pseudarthrosis Surgical fixation goals resection of pseudarthrosis to grossly normal bonecorrection of alignment bone grafting and stabilization of the remaining segments intramedullary splinting of the bone is desired techniques

Thanks Dr Vinit, yes psudoarthrosis in tibia is quite common, management explained very well,
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Neurofibromatosis ,since there are many abnormalities,which includes absence of radial muscles and nerves,it should be properly managed after assessment,and ulnar bone can be reconstructed with bone graft and plates leaving radial as such or removing it

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congenital pseudoarthrosis of forearm

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Recently published (2016) ,case report, open access

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