2 4-@dienoyl-coa reductase deficiency

Catalysis of the reaction: trans-2,3-didehydroacyl-CoA + NADP+ = trans,trans-2,3,4,5-tetradehydroacyl-CoA + NADPH + H+.

Disease Alternative Name

4-enoyl-coa reductase (nadph) activity
trans-2
3-didehydroacyl-coa:nadp+ 4-oxidoreductase activity
4-enoyl-coa reductase (nadph2)
4-enoyl coenzyme a (reduced nicotinamide adenine dinucleotide phosphate) reductase activity
4-enoyl-coa reductase activity
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