5-oxoprolinase deficiency

Catalysis of the reaction: 5-oxo-L-proline + ATP + 2 H(2)O = L-glutamate + ADP + 2 H(+) + phosphate.

Disease Alternative Name

5-opase activity
pyroglutamase (atp-hydrolysing)
pyroglutamic hydrolase activity
5-oxo-l-proline amidohydrolase (atp-hydrolysing)
pyroglutamate hydrolase activity
pyroglutamase activity
l-pyroglutamate hydrolase activity
5-oxoprolinase activity
pyroglutamase (atp-hydrolyzing) activity
oxoprolinase activity
5-oxo-l-prolinase activity
5-oxoprolinase (atp-hydrolysing)
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