Acetyl-coa alpha-glucosaminide n-acetyltransferase deficiency

Catalysis of the reaction: acetyl-CoA + heparan alpha-D-glucosaminide = CoA + heparan N-acetyl-alpha-D-glucosaminide.

Disease Alternative Name

acetyl-coa:heparan-alpha-d-glucosaminide n-acetyltransferase activity
acetyl-coa:alpha-glucosaminide n-acetyltransferase activity
heparin-alpha-glucosaminide n-acetyltransferase activity
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