Alpha-methyl-acetoacetyl-coa thiolase deficiency

Catalysis of the reaction: (R)-3-hydroxyacyl-CoA + NADP+ = 3-oxoacyl-CoA + NADPH + H+.

Disease Alternative Name

beta-ketoacyl-coa reductase
acetoacetyl coenzyme a reductase activity
d(-)-beta-hydroxybutyryl coa-nadp oxidoreductase activity
nadp-linked acetoacetyl coa reductase activity
short chain beta-ketoacetyl(acetoacetyl)-coa reductase activity
nadph:acetoacetyl-coa reductase activity
(r)-3-hydroxyacyl-coa dehydrogenase activity
d-3-hydroxyacyl-coa reductase activity
hydroxyacyl coenzyme-a dehydrogenase activity
(r)-3-hydroxyacyl-coa:nadp+ oxidoreductase activity
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