Malignant appendiceal glucagonoma

A glucagon-producing neuroendocrine tumor arising from the alpha cells of the pancreas. It may be associated with necrolytic erythema migrans, diarrhea, diabetes, glossitis, weight loss, malabsorption, and anemia. It displays vascular invasion and metastasizes to other anatomic sites.

Disease Alternative Name

malignant glucagonoma
alpha cell tumor
malignant
malignant pancreatic glucagonoma
glucagonoma
pancreatic alpha cell carcinoma
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