Case of the day

OHVIRA Syndrome (Obstructed Hemi-vagina and Ipsilateral Renal Anomaly)

Herlyn-Werner-Wunderlich syndrome is an unusual congenital anomaly of the female genitourinary system, which is described as uterine didelphys with Obstructed Hemi-vagina and Ipsilateral Renal Anomaly (OHIRA), also known as OHVIRA syndrome.




USG revealed uterine didelphys with right cavity showing echogenic mass filling up the entire right cavity with absent right kidney. Patient was taken up for MRI which showed uterine didelphys with biscollis. The right sided uterine cavity was filled with blood measuring upto 8.1 cm in length and 7.2 cm in the width and compressing the cervical canal of the left side with right sided hematometra with hematocolpos. Both ovaries appeared normal with no free fluid in the pelvis. The right kidney was absent and the left kidney showed mild hypertrophy.

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Rare conjenital anomaly wth.uterine didelphysus Surgical intervention wth vaginal constructions. Sir what are the usg finidings?

Thank you doctor

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