Concluded Case

Steven Johnson Disease

Recurrent oral mucosal ulceration with conjunctival mucosal involvement in a 12 yr old male child (2 episodes in 6 months) ,no skin involvement , with fever, respiratory distress. Associated with persistent mild anemia and leucopenia. No lymphadenopathy, splenomegaly present. All reports attached All clinical findings attached Kindly go through history, clinical examination and investigations. What's the diagnosis? Or D/D? ( other reports - Blood cultures negative , LFT -wnl, , RFT, electrolytes -wnl , only bilirubin 1mg/dl ) Our D/D : 1. SJS 2. Hereditary angioedema 3. Connective tissue disorder (unknown) 4. Immunodeficiency

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steven jhonson syndrome . extensive mucosa n submucosa of lips involved . do not use steroids . here esr is elevated hb is low pus cells in urine r/e send urine c/s too . i dont think there was a need for doing widal test n r/o malaria . its commonly caused by offending agents like sulphonamides anticonvulsants like carbamazepine nsaids . give whole fresh blood transfusion n IVIG . take opthalmic consultation . broad spectrum antibiotics mvi infusion .

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steven jhonson syndrome . extensive mucosa n submucosa of lips involved . do not use steroids . here esr is elevated hb is low pus cells in urine r/e send urine c/s too . i dont think there was a need for doing widal test n r/o malaria . its commonly caused by offending agents like sulphonamides anticonvulsants like carbamazepine nsaids . give whole fresh blood transfusion n IVIG . take opthalmic consultation . broad spectrum antibiotics mvi infusion .

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Sjs.......treatment according with steroids and supportive treat.

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Kawasaki leukaemia are DDS

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Behcets disease an autoimmune disease

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SJS

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Clinical features points towards steven johnson syndrome...

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SJS

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