Acylsphingosine deacylase deficiency

Catalysis of the reaction: 1-phosphatidyl-1D-myo-inositol + H(2)O = 1-acyl-sn-glycero-3-phospho-D-myo-inositol + a carboxylate + H(+).

Disease Alternative Name

1-phosphatidyl-d-myo-inositol 2-acylhydrolase activity
phosphatidylinositol phospholipase a2 activity
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