Alpha-mannosidase b deficiency

Catalysis of the hydrolysis of terminal, non-reducing alpha-D-mannose residues in alpha-D-mannosides.

Disease Alternative Name

alpha-d-mannosidase activity
alpha-d-mannoside mannohydrolase activity
alpha-d-mannopyranosidase activity
exo-alpha-mannosidase activity
1
2-alpha-mannosidase
p-nitrophenyl-alpha-mannosidase activity
2-alpha-d-mannosidase activity
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