Autoimmune lymphoproliferative syndrome type 1 autosomal dominant
An autoimmune hematologic disorder characterized by autoimmune hemolytic anemia, thrombocytopenia, lymphadenopathy, hepatomegaly and splenomegaly. Patients are at an increased risk of developing Hodgkin and non-Hodgkin lymphomas.
Disease Alternative Name
autoimmune lymphoproliferative syndrome
canale-smith syndrome
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