Autoimmune lymphoproliferative syndrome without fas mutations

An autoimmune hematologic disorder characterized by autoimmune hemolytic anemia, thrombocytopenia, lymphadenopathy, hepatomegaly and splenomegaly. Patients are at an increased risk of developing Hodgkin and non-Hodgkin lymphomas.

Disease Alternative Name

autoimmune lymphoproliferative syndrome
canale-smith syndrome
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